Cystic Fibrosis Related Diabetes: A Case Report

Abstract

Cystic fibrosis-related diabetes (CFRD) is a common complication of cystic fibrosis (CF). The main reason for CFRD is the increase of pancreatic damage in patients over the years, as well as the loss of pancreatic islet cells and the development of insulin deficiency. The purpose of treatment is to ensure normal growth and development in children and adolescents and to regulate blood glucose. The basis of the treatment is insulin therapy and medical nutrition therapy. Insulin therapy stabilizes lung function and improves nutritional status in patients with CFRD. A diet with high energy, high fat and high salt is recommended for patients with CFRD. Carbohydrate counting is useful in determining the pre-meal insulin dose in patients receiving insulin therapy. In this article, medical and medical nutritional therapy of the patient with CFRD, followed in our clinic, is presented with a review of the literature.